Pdf mortalidad por fibrosis quistica en chile 19972003. Primer consenso mexicano sobre fibrosis pulmonar idiopatica 34 neumol cir torax, vol. Fibrosis quistica diferencias epidemiologicas entre paises. The median survival and the quality of life of cystic fibrosis patients has increased remarkably in the last decades, changing from a lethal disease to a chronic disease, with a majority of patients in adult age, due to better knowledge of the pathology, precocious diagnosis, and preventive and aggressive management of the respiratory and nutritional complications, realised in specialized and multidisciplinary centers.
Feb 26, 2019 please use one of the following formats to cite this article in your essay, paper or report. Introduction this document is one of a series related to cystic fibrosis cf that have been published by who since 1983. Most documents report joint meetings and workshops organized by who in association with. Fibrosis quistica, epidemiologia, complicaciones, antibioticoterapia.
Pdf idiopathic pulmonary fibrosis ipf is a progressive and fatal disease. Fibrosis quistica, epidemiologia, complicaciones, antibiotico terapia. Various clinical phenotypes are influenced not only by the type of mutation found. Fibrosis quistica genetic and rare diseases information. Primer consenso mexicano sobre fibrosis pulmonar idiopatica. Cystic fibrosis cf is an autosomal recessive hereditary disease. Complications of cystic fibrosis can affect the respiratory, digestive and reproductive systems, as well as other organs. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. For many centuries, the disease was thought to be related to witchcraft and the evil eye and it was only in 1938 that dorothy h.
Desde entonces, han ocurrido importantes avances en. Early detection combined with early intervention measures have changed the course of this disease with improvements in their survival which has led to a growing population of patients 18 years. The median survival and the quality of life of cystic fibrosis patients has increased remarkably in the last decades, changing from a lethal disease to a chronic disease, with a majority of patients in adult age, due to better knowledge of the pathology, precocious diagnosis, and preventive and aggressive management of the respiratory and nutritional complications, realised in specialized and. Cystic fibrosis is an important pediatric problem due to its high and premature mortality, to the deficient quality of life it generates in the patients and to the absence of a curative treatment. Cystic fibrosis is the most common lifeshortening recessively inherited disorder in the caucasian population. The genetic mutation that most frequently provokes cystic fibrosis.
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